@article { author = {Abolhassani, Hassan and Tavakol, Marzieh and Chavoshzadeh, Zahra and Mahdaviani, Seyed Alireza and Momen, Tooba and Yazdani, Reza and Azizi, Gholamreza and Movahedi, Masoud and Hamidieh, Amir Ali and Behniafard, Nasrin and Nabavi, Mohammamd and Arshi, Saba and Bemanian, Mohammad Hassan and Fallahpour, Morteza and Shokri, Sima and Molatefi, Rasol and Sherkat, Roya and Shirkani, Afshin and Amin, Reza and Aleyasin, Soheila and Faridhosseini, Reza and Jabbari-Azad, Farahzad and Mohammadzadeh, Iraj and Ghaffari, Javad and Shafiei, Alireza and Kalantari, Arash and Mansouri, Mahboubeh and Mesdaghi, Mehrnaz and Babaie, Delara and Ahanchian, Hamid and Khoshkhui, Maryam and Soheili, Habib and Eslamian, Mohammad Hossein and Cheraghi, Taher and Dabbaghzadeh, Abbas and Tavassoli, Mahmoud and Nasiri Kalmarzi, Rasoul and Mortazavi, Seyed Hamidreza and Kashef, Sara and Esmaeilzadeh, Hossein and Tafaroji, Javad and Khalili, Abbas and Zandieh, Fariborz and Sadeghi-Shabestari, Mahnaz and Darougar, Sepideh and Behmanesh, Fatemeh and Akbari, Hedayat and Zandkarimi, Mohammadreza and Abolnezhadian, Farhad and Fayezi, Abbas and Moghtaderi, Mojgan and Ahmadiafshar, Akefeh and Shakerian, Behzad and Sajedi, Vahid and Taghvaei, Behrang and Safari, Mojgan and Heidarzadeh, Marzieh and Ghalehbaghi, Babak and Fathi, Seyed Mohammad and Darabi, Behzad and Bazregari, Saeed and Bazargan, Nasrin and Khayatzadeh, Alireza and Javahertrash, Naser and Bashardoust, Bahram and Zamani, Mohammadali and Mohsenzadeh, Azam and Ebrahimi, Sarehsadat and Sharafian, Samin and Vosughimotlagh, Ahmad and Tafakoridelbari, Mitra and Rahimi, Maziar and Ashournia, Parisa and Razaghian, Anahita and Aghaeimeybodi, Fatemeh and Mamishi, Setareh and Parvaneh, Nima and Rezaei, Nima and Aghamohammadi, Asghar}, title = {National Consensus on Diagnosis and Management Guidelines for Primary Immunodeficiency}, journal = {Immunology and Genetics Journal}, volume = {2}, number = {1}, pages = {1-21}, year = {2019}, publisher = {Research Center For Immunodeficiencies}, issn = {2645-4831}, eissn = {2645-4831}, doi = {10.22034/igj.2019.85743}, abstract = {Primary immunodeficiency (PID) is a group of more than 400 distinct genetic disorders affecting both children and adults. As signs and symptoms of PID are usually heterogeneous and unspecific, based on the available human resources and laboratory facilities, diagnosis and follow-up of these patients can be challenging. In line with this notion, management and treatment of PID are practiced divergently in different PID centers. In order to reach a distinct national protocol and given the little evidence on appropriate or universal guidelines to improve the current status of management of the disease, the Iranian PID network designed a consensus suitable for regional resources. This review summarizes this PID guideline based on the importance of different clinical complications and the level of medical authority visiting those at the first line. Further, for each complication, appropriate interventions are mentioned to improve the approach.}, keywords = {Primary immunodeficiency,Symptoms,Management,consensus,guideline}, url = {http://www.igjournal.ir/article_85743.html}, eprint = {http://www.igjournal.ir/article_85743_6ca16a5014f35825bb847691970b005f.pdf} }